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DeCS
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Descriptor English:
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Coproporphyrinogen Oxidase
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Descriptor Spanish:
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Coproporfirinógeno Oxidasa
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Descriptor Portuguese:
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Coproporfirinogênio Oxidase
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Synonyms English:
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Coproporphyrinogenase
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Tree Number:
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D08.811.682.660.250
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Definition English:
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An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA. |
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Entry Combination - descr/qualif English:
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Coproporphyrinogen Oxidase/deficiency use Porphyrias, Hepatic
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History Note English:
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91(76); was see under OXIDOREDUCTASES 1976-90
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Allowable Qualifiers English:
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Record Number:
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3324
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Unique Identifier:
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D003304
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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